27 Jun Find out what the seizures look like, how it’s diagnosed and treated, and the outlook for people with this rare epilepsy with a progressive loss of. Este síndrome podría estar significativamente subdiagnosticado, si se consideran sus características, muy variables, que incluyen trastornos de atención, del. Landau–Kleffner syndrome (LKS)—also called infantile acquired aphasia, acquired epileptic aphasia or aphasia with convulsive disorder—is a rare childhood.

Author: Tokasa Zololkree
Country: Suriname
Language: English (Spanish)
Genre: Travel
Published (Last): 21 December 2014
Pages: 33
PDF File Size: 5.53 Mb
ePub File Size: 5.58 Mb
ISBN: 226-4-77786-329-2
Downloads: 81679
Price: Free* [*Free Regsitration Required]
Uploader: Mikagul

Mikati MA, Saab R.

Landau–Kleffner syndrome

Occasionally, the condition may be induced secondary to other diagnoses such as low-grade brain tumors, closed-head injury, neurocysticercosisand demyelinating disease. We observed significant symptom improvement when flunarizine was added to the treatment.

Speech therapy begins immediately at the time of diagnosis along with medical treatment that may include steroids and anti-epileptic or anti-convulsant medications. Seizures Simple partial Complex partial Gelastic seizure Epilepsy Temporal kkleffner epilepsy Frontal lobe epilepsy Rolandic epilepsy Nocturnal epilepsy Panayiotopoulos syndrome.

Pediatr Neurol ; However, acute onset of the condition has also been reported as well as episodic aphasia. Engel J, Pedley TA, eds. Another 4 of the 14 displayed improvement of speech and understanding instructions given verbally, but they still required speech therapy. The electrical status epilepticus syndrome. On long-term followup, most of his patients did not demonstrate total epilepsy remission and language problems continued.


There appears to be a male landu in the diagnosis of the syndrome ratio of 1.

Uso de flunarizina en un caso con síndrome de Landau-Kleffner

Double-blind placebo-controlled trial of flunarizine as add-on therapy in epilepsy. Regional cerebral perfusion in Landau-Kleffner syndrome and related childhood aphasias. Seizures generally disappear by landsu.

Acquired epileptiform aphasia in children Landau-Kleffner syndrome. Seven of the fourteen patients recovered age-appropriate speech and no longer required speech therapy.

Instead, there are reports that indicate that treatment with high-dose corticosteroids during early stages of the disease improves the speech difficulties. Epilepsy with continuous spike-waves during slow sleep and its treatment. Treatment with subpial intracortical transection. The cortex is sindgome in parallel lines to the midtemporal gyrus and perisylvian area to attenuate the spread of the epileptiform activity without causing cortical dysfunction.

Developmental dyslexia Dyscalculia Dysgraphia Disorder of written expression.

Electrical status epilepticus during slow-wave sleep: Views Read Edit View history. A pharmacologic study of five cases.


Landau-Kleffner and autistic regression: the importance of differential diagnosis

He has not had seizures for a year. Acquired epileptic aphasia, verbal auditive agnosia, epileptic encephalopathy, Landau-Kleffner’s syndrome. Late onset acquired epileptic aphasia. Landau-Kleffner and autistic regression: O paciente recebeu alta para acompanhamento ambulatorial, com melhora relativa do quadro comportamental e da linguagem.

Antecedentes prenatales y perinatales: Pulse methylprednisolone therapy in Landau-Kleffner syndrome. We stress the main differences between these two entities because misdiagnosis may postpone early intervention and consequent benefits, as observed in our case. The prognosis for children with LKS varies. Epilepsy types Specific developmental disorders Syndromes.

Page not available

Electrical status epilepticus during sleep ESES. Can J Neurol Sci ; The prognosis is improved when the onset of the disorder is after age 6 and when speech therapy is started early. J Clin Neurophysiol ;8: